A. Respiratory Function (Crucial)

Do not rely on “feeling breathless.” Use a digital home spirometer to record objective pulmonary data.

• FVC (Forced Vital Capacity): Record the numerical value (Liters) weekly.
• SpO2 (Blood Oxygen Saturation): Monitor daily using a pulse oximeter, especially post-intervention.

B. Bulbar Function & Articulation

Subjective listening is unreliable due to daily fluctuations. Create chronological audio records.

• Phonation Testing: Record the patient speaking specific consonant sounds (e.g., “Sa”, “Ra”) and a standardized short sentence once a week.
• Swallowing Observation: Log the frequency of choking incidents per meal.

C. Motor Function & Extremities

• Grip Strength: Measure using a digital dynamometer (kg/lbs) bi-weekly.
• Range of Motion (ROM): Record video of maximum limb elevation (e.g., raising arms, lifting legs while seated) from a fixed camera angle.

A. Physical Muscle Volume

Visual estimation is insufficient. Use a measuring tape at consistent anatomical landmarks.

• Circumference Measurement: Measure thighs, calves, and upper arms at the exact same point (e.g., 15cm above the patella) bi-weekly.

B. Gait & Core Stability

• Fall Frequency: Strictly log the number of falls or near-falls per week.
• Timed Walk Test: Measure the time (in seconds) it takes to walk a flat, straight 10-meter (33 ft) distance.
• Postural Video: Record standing posture and gait mechanics from the front and side to observe shifts in pelvic stability and lordosis.

C. Specific ROM (e.g., FSHD)

• Scapular Mobility: Document the maximum angle of shoulder elevation and the physical movement of the scapula through video tracking.